Would just a little bit of a drink (of alcohol) be ok?

Even a little bit of drinking can cause serious damage.

There are many  AACD* patients who had an onset following the consumption of alcoholic beverages. The hard limit can depend on the person on a particular day but in citrin deficiency, even a small amount can cause devastating damage to a patient, including abnormal behaviors and encephalopathy, which can be life-threatening.

It is too risky to test your limits.

*Adolescent and adult-onset citrin deficiency (AACD) – formerly known as CTLN2