Patients are advised to eat the food they desire when he/she does not have an appetite. Seek treatment if the condition persists or if they feel too sick to eat or drink, as their condition is likely to develop into hypoglycemia.

If you are worried about hypoglycemia, you can discuss with your doctor on using glucose meters that you can use at home.

In case of treating pain or fever at home, please remember that significant excess of the prescribed amount/period of acetaminophen intake is said to damage liver of citrin deficiency patients.

Some medicine may be too sweet for the patients. Parents could use a compounding pharmacy to make non-sweet liquids, ask for suppositories or tablets and crush the tablets, or add water to dilute the medicine to help patients take medication.

If a patient sees a doctor other than the attending doctor, please tell him/her that the patient has citrin deficiency. There is no problem with temporary general glucose infusion for the treatment of hypoglycemia and general infusion for the treatment of diarrhea or vomiting. It is advisable to let patients eat/drink what they wish regardless of the general medical protocol for a quicker recovery after their appetite returns.

If you are losing weight and/or experiencing somnolence, please consult your doctor.